Quantity size:
0.2ml
Concentration:
1mg/ml 溶质载体家族19成员3抗体 Buffer = Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4
Background:
This gene encodes a ubiquitously expressed transmembrane thiamine transporter that lacks folate transport activity. Mutations in this gene cause biotin-responsive basal ganglia disease (BBGD); a recessive disorder manifested in childhood that progresses to chronic encephalopathy, dystonia, quadriparesis, and death if untreated. Patients with BBGD have 溶质载体家族19成员3抗体 bilateral necrosis in the head of the caudate nucleus and in the putamen. Administration of high doses of biotin in the early progression of the disorder eliminates pathological symptoms while delayed treatment results in residual paraparesis, mild mental retardation, or dystonia. 溶质载体家族19成员3抗体 Administration of thiamine is ineffective in the treatment of this disorder. Experiments have failed to show that this protein can transport biotin. Mutations in this gene also cause a Wernicke's-like encephalopathy.[provided by RefSeq, Jan 2010]
溶质载体家族19成员3抗体 Also known as:
Solute carrier family 19 member 3; Thiamine transporter 2; thTr 2; THTR2.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, .
●
Immunogen: KLH conjugated synthetic peptide derived from human SLC19A3.
●
Predicted Molecular Weight: 56kDa.
溶质载体家族19成员3抗体 Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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kl355Mu01甲状腺球蛋白(TG)多克隆抗体Polyclonal Antibody to Thyroglobulin (TG)
kl355Ra01甲状腺球蛋白(TG)多克隆抗体Polyclonal Antibody to Thyroglobulin (TG)
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kl037Hu01纤连蛋白(FN)多克隆抗体Polyclonal Antibody to Fibronectin (FN)
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kl184Hu01粘蛋白21(MUC21)多克隆抗体Polyclonal Antibody to Mucin 21 (MUC21)
kl995Hu01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
kl995Mu01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
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kl403Bo01粘蛋白17(MUC17)多克隆抗体Polyclonal Antibody to Mucin 17 (MUC17)
kl808Hu01粘蛋白7(MUC7)多克隆抗体Polyclonal Antibody to Mucin 7, Secreted (MUC7)
kl808Bo01粘蛋白7(MUC7)多克隆抗体Polyclonal Antibody to Mucin 7, Secreted (MUC7)
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企业名称
上海康朗生物科技有限公司
企业信息已认证
企业类型
信用代码
310112001510759
成立日期
2015-05-29
注册资本
100
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上海康朗生物科技有限公司
公司地址
上海市闵行区闵北路88弄1-30号第22栋BV145室
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