Quantity size:
0.2ml
Concentration:
1mg/ml 过氧化物酶体生物合成因子5抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
The product of this gene binds to the C-terminal PTS1-type tripeptide peroxisomal targeting signal (SKL-type) and plays an essential role in peroxisomal protein import. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome 过氧化物酶体生物合成因子5抗体function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of过氧化物酶体生物合成因子5抗体 neonatal adrenoleukodystrophy (NALD), a cause of Zellweger syndrome (ZWS) as well as may be a cause of infantile Refsum disease (IRD). Alternatively spliced transcript variants encoding different isoforms have been identified. [provided by RefSeq, Oct 2008]
Also known as:
FLJ50634; FLJ50721; FLJ51948; Peroxin 5; Peroxin-5; Peroxisomal biogenesis factor 5; Peroxisomal C terminal过氧化物酶体生物合成因子5抗体 targeting signal import receptor; Peroxisomal C-terminal targeting signal import receptor; Peroxisomal targeting signal 1 receptor; Peroxisome receptor 1; pex5; PEX5_HUMAN; PTS1 BP; PTS1 receptor; PTS1-BP; PTS1R; PXR1.
Specificity:
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Rabbit Polyclonal IgG, affinity purified by Protein A.
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Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Sheep, .
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Immunogen: KLH conjugated synthetic peptide derived from human PEX5.
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过氧化物酶体生物合成因子5抗体Predicted Molecular Weight: 71kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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kl235Hu01补体1抑制因子(C1INH)多克隆抗体Polyclonal Antibody to Complement 1 Inhibitor (C1INH)
kl235Mu01补体1抑制因子(C1INH)多克隆抗体Polyclonal Antibody to Complement 1 Inhibitor (C1INH)
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kl238Ra01酪氨酸酶(TYR)多克隆抗体Polyclonal Antibody to Tyrosinase (TYR)
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kl243Mu01对氧磷酶1(PON1)多克隆抗体Polyclonal Antibody to klaoxonase 1 (PON1)
kl243Ra01对氧磷酶1(PON1)多克隆抗体Polyclonal Antibody to klaoxonase 1 (PON1)
kl244Hu01胱天蛋白酶2(CASP2)多克隆抗体Polyclonal Antibody to Caskle 2 (CASP2)
kl249Hu01Nischarin蛋白(NISCH)多克隆抗体Polyclonal Antibody to Nischarin (NISCH)
kl252Bo01载脂蛋白C1(APOC1)多克隆抗体Polyclonal Antibody to Apolipoprotein C1 (APOC1)
kl252Ca01载脂蛋白C1(APOC1)多克隆抗体Polyclonal Antibody to Apolipoprotein C1 (APOC1)
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kl252Mu01载脂蛋白C1(APOC1)多克隆抗体Polyclonal Antibody to Apolipoprotein C1 (APOC1)
企业名称
上海康朗生物科技有限公司
企业信息已认证
企业类型
信用代码
310112001510759
成立日期
2015-05-29
注册资本
100
经营范围
从事生物科技技术领域内技术开发、技术咨询、技术服务、技术转让,实验分析仪器、化工产品及原料(除危险化学品、监控化学品、烟花爆竹、民用爆竹物品、易制毒化学品)、仪器仪表、环保设备、酒店用品、皮革制品、床上用品、电子产品的销售。【依法须经批准的项目,经相关部门批准后方可开展经营活动】
上海康朗生物科技有限公司
公司地址
上海市闵行区闵北路88弄1-30号第22栋BV145室
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