Quantity size:
0.2ml
Concentration:
1mg/ml 丙酮酸脱氢酶E2抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes component E2 of the multi-enzyme pyruvate dehydrogenase complex (PDC). PDC resides in the inner mitochondrial membrane and catalyzes the conversion of pyruvate to acetyl coenzyme A. The protein product of this gene, dihydrolipoamide acetyltransferase, accepts acetyl groups formed by the oxidative decarboxylation of pyruvate and transfers them to coenzyme A. Dihydrolipoamide acetyltransferase is the antigen 丙酮酸脱氢酶E2抗体for antimitochondrial antibodies. These autoantibodies are present in nearly 95% of patients with the autoimmune liver disease primary biliary cirrhosis (PBC). In PBC, activated T lymphocytes attack and destroy epithelial cells in the bile duct where this protein is abnormally distributed and overexpressed. PBC enventually leads to cirrhosis and liver failure. Mutations in this gene are also a cause of pyruvate dehydrogenase E2 deficiency which causes primary lactic acidosis in infancy and early childhood.[provided by RefSeq, Oct 2009]
丙酮酸脱氢酶E2抗体Also known as:
Pyruvate Dehydrogenase E2; 70 kDa mitochondrial autoantigen of primary biliary cirrhosis; anti DLAT; Dihydrolipoamide acetyltransferase component of pyruvate dehydrogenase complex; Dihydrolipoamide; Dihydrolipoamide S Acetyltransferase; Dihydrolipoamide S-acetyltransferase (E2 component of pyruvate dehydrogenase complex); Dihydrolipoamide S-Acetyltransferase; Dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex; dihydrolipoyllysine-residue acetyltransferase component of pyruvate dehydrogenase complex mitochondrial; DLAT; DLTA; E2;丙酮酸脱氢酶E2抗体 E2 component of pyruvate dehydrogenase complex; EC 2.3.1.12; M2 antigen complex 70 kDa subunit; M2 Antigen Complex 70kD Subunit; mitochondrial; ODP2_HUMAN; PBC; PDC E2; PDC-E2; PDCE2; Pyruvate dehydrogenase complex component E2; Pyruvate dehydrogenase complex E2 subunit; S acetyltransferase component of pyruvate dehydrogenase complex.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: 丙酮酸脱氢酶E2抗体Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, Zebrafish, Sheep, Guinea Pig, Cat, ,Danio rerio.
●
Immunogen: KLH conjugated synthetic peptide derived from human PDCE2.
●
Predicted Molecular Weight: 63kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
l518Hu01铁蛋白(FE)多克隆抗体Polyclonal Antibody to Ferritin (FE)
kl518Mu01铁蛋白(FE)多克隆抗体Polyclonal Antibody to Ferritin (FE)
kl518Ra01铁蛋白(FE)多克隆抗体Polyclonal Antibody to Ferritin (FE)
kl355Hu01甲状腺球蛋白(TG)多克隆抗体Polyclonal Antibody to Thyroglobulin (TG)
kl355Mu01甲状腺球蛋白(TG)多克隆抗体Polyclonal Antibody to Thyroglobulin (TG)
kl355Ra01甲状腺球蛋白(TG)多克隆抗体Polyclonal Antibody to Thyroglobulin (TG)
kl821Mu01C反应蛋白(CRP)多克隆抗体Polyclonal Antibody to C Reactive Protein (CRP)
kl821Ra01C反应蛋白(CRP)多克隆抗体Polyclonal Antibody to C Reactive Protein (CRP)
kl216Hu01绒毛膜促性腺激素(CG)多克隆抗体Polyclonal Antibody to Chorionic Gonadotropin (CG)
kl930Hu01脱铁转铁蛋白(apoTf)多克隆抗体Polyclonal Antibody to Apotransferrin (apoTf)
kl037Hu01纤连蛋白(FN)多克隆抗体Polyclonal Antibody to Fibronectin (FN)
kl037Mu01纤连蛋白(FN)多克隆抗体Polyclonal Antibody to Fibronectin (FN)
kl037Ra01纤连蛋白(FN)多克隆抗体Polyclonal Antibody to Fibronectin (FN)
kl082Hu01层粘连蛋白(LN)多克隆抗体Polyclonal Antibody to Laminin (LN)
kl082Ra01层粘连蛋白(LN)多克隆抗体Polyclonal Antibody to Laminin (LN)
kl184Hu01粘蛋白21(MUC21)多克隆抗体Polyclonal Antibody to Mucin 21 (MUC21)
kl995Hu01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
kl995Mu01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
kl995Ra01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
kl995Bo01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
kl403Hu01粘蛋白17(MUC17)多克隆抗体Polyclonal Antibody to Mucin 17 (MUC17)
kl403Bo01粘蛋白17(MUC17)多克隆抗体Polyclonal Antibody to Mucin 17 (MUC17)
更多
企业名称
上海康朗生物科技有限公司
企业信息已认证
企业类型
信用代码
310112001510759
成立日期
2015-05-29
注册资本
100
经营范围
从事生物科技技术领域内技术开发、技术咨询、技术服务、技术转让,实验分析仪器、化工产品及原料(除危险化学品、监控化学品、烟花爆竹、民用爆竹物品、易制毒化学品)、仪器仪表、环保设备、酒店用品、皮革制品、床上用品、电子产品的销售。【依法须经批准的项目,经相关部门批准后方可开展经营活动】
上海康朗生物科技有限公司
公司地址
上海市闵行区闵北路88弄1-30号第22栋BV145室
客服电话