Quantity size:
0.2ml
Concentration:
1mg/ml 肌动蛋白结合蛋白Z盘状蛋白抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Nebulette binds to actin and plays an important role in Z-disk assembly. It is a cardiac homolog of nebulin and its expression is abundant in cardiac muscle. Nebulette defects are assocated with non-familial idiopathic cardiacmyopathy.
Nebulin and nebulette are homologous 肌动蛋白结合蛋白Z盘状蛋白抗体 thin-filament associated proteins expressed in skeletal and cardiac muscles, respectively. Nebulette, unlike nebulin, is confined to the Z-disc region of the sarcomere and does not span the whole thin filament length. Nebulette colocalizes with α-actinin in the pre-, nascent, and mature myofibrils. A polymorphism in the actin-binding motif of nebulette is a肌动蛋白结合蛋白Z盘状蛋白抗体 genetic marker of susceptibility to nonfamilial idiopathic dilated cardiomyopathy (IDC), characterized by a thin-walled heart and systolic dysfunction.
肌动蛋白结合蛋白Z盘状蛋白抗体 Also known as:
Actin binding Z disk protein; bA56H7.1; LIM nebulette; LNEBL; NEBL; NEBL_HUMAN.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, .
●
Immunogen: KLH conjugated synthetic peptide derived from human Nebulette.
●
肌动蛋白结合蛋白Z盘状蛋白抗体 Predicted Molecular Weight: 116kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
kl340Hu01蛛毒素受体3(LPHN3)多克隆抗体Polyclonal Antibody to Latrophilin 3 (LPHN3)
kl344Hu01回肠脂肪酸结合蛋白(FABP6)多克隆抗体Polyclonal Antibody to Fatty Acid Binding Protein 6, Ileal (FABP6)
kl344Mu01回肠脂肪酸结合蛋白(FABP6)多克隆抗体Polyclonal Antibody to Fatty Acid Binding Protein 6, Ileal (FABP6)
kl347Hu01着丝粒蛋白F(CENPF)多克隆抗体Polyclonal Antibody to Centromere Protein F (CENPF)
kl350Mu01Ⅰ型胶原α1(COL1α1)多克隆抗体Polyclonal Antibody to Collagen Type I Alpha 1 (COL1a1)
kl350Ra01Ⅰ型胶原α1(COL1α1)多克隆抗体Polyclonal Antibody to Collagen Type I Alpha 1 (COL1a1)
kl357Hu01成纤维细胞生长因子5(FGF5)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor 5 (FGF5)
kl362Hu01尾加压素2(UST2)多克隆抗体Polyclonal Antibody to Urotensin 2 (UST2)
kl363Hu01血小板内皮细胞粘附分子1(PECAM1)多克隆抗体Polyclonal Antibody to Platelet/Endothelial Cell Adhesion Molecule (PECAM1)
kl363Mu01血小板内皮细胞粘附分子1(PECAM1)多克隆抗体Polyclonal Antibody to Platelet/Endothelial Cell Adhesion Molecule (PECAM1)
kl363Ra01血小板内皮细胞粘附分子1(PECAM1)多克隆抗体Polyclonal Antibody to Platelet/Endothelial Cell Adhesion Molecule (PECAM1)
kl370Hu01β-血小板球蛋白(βTG)多克隆抗体Polyclonal Antibody to Beta-Thromboglobulin (bTG)
kl370Mu01β-血小板球蛋白(βTG)多克隆抗体Polyclonal Antibody to Beta-Thromboglobulin (bTG)
kl370Ra01β-血小板球蛋白(βTG)多克隆抗体Polyclonal Antibody to Beta-Thromboglobulin (bTG)
kl371Bo0110kDa干扰素γ诱导蛋白(IP10)多克隆抗体Polyclonal Antibody to Interferon Gamma Induced Protein 10kDa (IP10)
kl371Ca0110kDa干扰素γ诱导蛋白(IP10)多克隆抗体Polyclonal Antibody to Interferon Gamma Induced Protein 10kDa (IP10)
kl371Hu0110kDa干扰素γ诱导蛋白(IP10)多克隆抗体Polyclonal Antibody to Interferon Gamma Induced Protein 10kDa (IP10)
kl371Mu0110kDa干扰素γ诱导蛋白(IP10)多克隆抗体Polyclonal Antibody to Interferon Gamma Induced Protein 10kDa (IP10)
kl371Ra0110kDa干扰素γ诱导蛋白(IP10)多克隆抗体Polyclonal Antibody to Interferon Gamma Induced Protein 10kDa (IP10)
kl373Hu01结蛋白(Des)多克隆抗体Polyclonal Antibody to Desmin (Des)
kl373Mu01结蛋白(Des)多克隆抗体Polyclonal Antibody to Desmin (Des)
kl373Ra01结蛋白(Des)多克隆抗体Polyclonal Antibody to Desmin (Des)
kl374Ra01GATA结合蛋白4(GATA4)多克隆抗体Polyclonal Antibody to GATA Binding Protein 4 (GATA4)
kl376Hu01辅肌动蛋白α2(ACTN2)多克隆抗体Polyclonal Antibody to Actinin Alpha 2 (ACTN2)
kl376Mu01辅肌动蛋白α2(ACTN2)多克隆抗体Polyclonal Antibody to Actinin Alpha 2 (ACTN2)
kl380Bo01血管活性肠肽(VIP)多克隆抗体Polyclonal Antibody to Vasoactive Intestinal Peptide (VIP)
kl380Hu01血管活性肠肽(VIP)多克隆抗体Polyclonal Antibody to Vasoactive Intestinal Peptide (VIP)
更多
企业名称
上海康朗生物科技有限公司
企业信息已认证
企业类型
信用代码
310112001510759
成立日期
2015-05-29
注册资本
100
经营范围
从事生物科技技术领域内技术开发、技术咨询、技术服务、技术转让,实验分析仪器、化工产品及原料(除危险化学品、监控化学品、烟花爆竹、民用爆竹物品、易制毒化学品)、仪器仪表、环保设备、酒店用品、皮革制品、床上用品、电子产品的销售。【依法须经批准的项目,经相关部门批准后方可开展经营活动】
上海康朗生物科技有限公司
公司地址
上海市闵行区闵北路88弄1-30号第22栋BV145室
客服电话