Quantity size:
0.2ml
Concentration:
1mg/ml NADH脱氢酶黄素蛋白1抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
The mitochondrial respiratory chain provides energy to cells via oxidative phosphorylation and consists of four membrane-bound electron-transporting protein complexes (I-IV) and an ATP synthase (complex V). This gene encodes a 51 kDa subunit of the NADH:ubiquinone oxidoreductase complex I; a large complex with at least 45 nuclear and mitochondrial encoded subunits that liberates electrons from NADH and channels them to ubiquinoneNADH脱氢酶黄素蛋白1抗体. This subunit carries the NADH-binding site as well as flavin mononucleotide (FMN)- and Fe-S-biding sites. Defects in complex I are a common cause of mitochondrial dysfunction; a syndrome that occurs in approximately 1 in 10,000 live births. Mitochondrial complex I deficiencyNADH脱氢酶黄素蛋白1抗体 is linked to myopathies, encephalomyopathies, and neurodegenerative disorders such as Parkinson's disease and Leigh syndrome. Alternative splicing results in multiple transcript variants encoding distinct isoforms.[provided by RefSeq, Oct 2009]
Also known as:
CI 51kD; Complex I 51kD; NADH dehydrogenase (ubiquinone) flavoprotein 1; NADH dehydrogenase [ubiquinone] flavoprotein 1, mitochondrial; NADH dehydrogenase flavoprotein 1; NADH脱氢酶黄素蛋白1抗体NADH ubiquinone oxidoreductase 51 kDa subunit; NADH ubiquinone oxidoreductase; NDUFV 1; UQOR1; NDUV1_HUMAN.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, .
●
Immunogen: KLH conjugated synthetic peptide derived from human NDUFV1.
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Predicted Molecular Weight: 49kDa.
NADH脱氢酶黄素蛋白1抗体Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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kl243Ra01心型脂肪酸结合蛋白(FABP3)多克隆抗体Polyclonal Antibody to Fatty Acid Binding Protein 3, Muscle And Heart (FABP3)
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kl252Mu01雄激素受体(AR)多克隆抗体Polyclonal Antibody to Androgen Receptor (AR)
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kl258Ra01谷氨酸脱羧酶2(GAD2)多克隆抗体Polyclonal Antibody to Glutamate Decarboxylase 2, Acid (GAD2)
kl261Hu01CD72分子(CD72)多克隆抗体Polyclonal Antibody to Cluster Of Differentiation 72 (CD72)
kl262Hu01整合素β3(ITGβ3)多克隆抗体Polyclonal Antibody to Integrin Beta 3 (ITGb3)
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kl265Hu01胰多肽(PP)多克隆抗体Polyclonal Antibody to klcreatic Polypeptide (PP)
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上海康朗生物科技有限公司
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信用代码
310112001510759
成立日期
2015-05-29
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100
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