Quantity size:
0.1ml
Concentration:
1mg/ml 磷酸化低密度脂蛋白受体相关蛋白5抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
LRP5 is involved in the Wnt/beta catenin signaling pathway, probably by acting as a coreceptor together with Frizzled for Wnt. Defects in LRP5 are a cause of autosomal dominant and autosomal recessive familial exudative vitreoretinopathy (FEVR). Autosomal dominant FEVR is also referred to as exudative vitreoretinopathy 1 (EVR1); also known as Criswick-Schepens syndrome. FEVR is a disorder of the retinal vasculature characterized by an磷酸化低密度脂蛋白受体相关蛋白5抗体 abrupt cessation of growth of peripheral capillaries, leading to an avascular peripheral retina. This may lead to compensatory retinal neovascularization, which is thought to be induced by hypoxia from the initial avascular insult. New vessels are prone to leakage and rupture causing exudates and bleeding, followed by scarring, retinal detachment and blindness. FEVR is reported to have a penetrance of 100%, but clinical features can 磷酸化低密度脂蛋白受体相关蛋白5抗体be highly variable, even within the same family. Patients with mild forms of the disease are asymptomatic, and their only disease-related abnormality is an arc of avascular retina in the extreme temporal periphery.
磷酸化低密度脂蛋白受体相关蛋白5抗体Also known as:
BMND1; HBM; HGNC:6697; Low density lipoprotein receptor related protein 5; Low density lipoprotein receptor related protein 7; Low-density lipoprotein receptor-related protein 5; LR3; LRP-5; Lrp5; LRP5_HUMAN; LRP7; OPPG; OPS; Osteoporosis pseudoglioma syndrome; VBCH2.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
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Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, .
●
Immunogen: KLH conjugated Synthesised phosphopeptide derived from human.
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Predicted Molecular Weight: 176kDa.
磷酸化低密度脂蛋白受体相关蛋白5抗体Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
kl808Bo01粘蛋白7(MUC7)多克隆抗体Polyclonal Antibody to Mucin 7, Secreted (MUC7)
kl489Hu01粘蛋白6(MUC6)多克隆抗体Polyclonal Antibody to Mucin 6 (MUC6)
kl489Mu01粘蛋白6(MUC6)多克隆抗体Polyclonal Antibody to Mucin 6 (MUC6)
kl489Bo01粘蛋白6(MUC6)多克隆抗体Polyclonal Antibody to Mucin 6 (MUC6)
kl684Hu01粘蛋白5B(MUC5B)多克隆抗体Polyclonal Antibody to Mucin 5 Subtype B (MUC5B)
kl684Mu01粘蛋白5B(MUC5B)多克隆抗体Polyclonal Antibody to Mucin 5 Subtype B (MUC5B)
kl684Bo01粘蛋白5B(MUC5B)多克隆抗体Polyclonal Antibody to Mucin 5 Subtype B (MUC5B)
kl756Hu01粘蛋白5AC(MUC5AC)多克隆抗体Polyclonal Antibody to Mucin 5 Subtype AC (MUC5AC)
kl756Mu01粘蛋白5AC(MUC5AC)多克隆抗体Polyclonal Antibody to Mucin 5 Subtype AC (MUC5AC)
kl756Ra01粘蛋白5AC(MUC5AC)多克隆抗体Polyclonal Antibody to Mucin 5 Subtype AC (MUC5AC)
kl756Bo01粘蛋白5AC(MUC5AC)多克隆抗体Polyclonal Antibody to Mucin 5 Subtype AC (MUC5AC)
kl034Hu01粘蛋白4(MUC4)多克隆抗体Polyclonal Antibody to Mucin 4 (MUC4)
kl034Mu01粘蛋白4(MUC4)多克隆抗体Polyclonal Antibody to Mucin 4 (MUC4)
kl034Ra01粘蛋白4(MUC4)多克隆抗体Polyclonal Antibody to Mucin 4 (MUC4)
kl034Bo01粘蛋白4(MUC4)多克隆抗体Polyclonal Antibody to Mucin 4 (MUC4)
kl031Hu01粘蛋白3(MUC3)多克隆抗体Polyclonal Antibody to Mucin 3 (MUC3)
kl031Mu01粘蛋白3(MUC3)多克隆抗体Polyclonal Antibody to Mucin 3 (MUC3)
kl031Ra01粘蛋白3(MUC3)多克隆抗体Polyclonal Antibody to Mucin 3 (MUC3)
kl031Bo01粘蛋白3(MUC3)多克隆抗体Polyclonal Antibody to Mucin 3 (MUC3)
kl705Hu01粘蛋白2(MUC2)多克隆抗体Polyclonal Antibody to Mucin 2 (MUC2)
kl705Mu01粘蛋白2(MUC2)多克隆抗体Polyclonal Antibody to Mucin 2 (MUC2)
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企业名称
上海康朗生物科技有限公司
企业信息已认证
企业类型
信用代码
310112001510759
成立日期
2015-05-29
注册资本
100
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从事生物科技技术领域内技术开发、技术咨询、技术服务、技术转让,实验分析仪器、化工产品及原料(除危险化学品、监控化学品、烟花爆竹、民用爆竹物品、易制毒化学品)、仪器仪表、环保设备、酒店用品、皮革制品、床上用品、电子产品的销售。【依法须经批准的项目,经相关部门批准后方可开展经营活动】
上海康朗生物科技有限公司
公司地址
上海市闵行区闵北路88弄1-30号第22栋BV145室
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