Quantity size:
0.2ml
Concentration:
1mg/ml 低密度脂蛋白受体相关蛋白5抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
LRP5 is involved in the Wnt/beta catenin signaling pathway, probably by acting as a coreceptor together with Frizzled for Wnt. Defects in LRP5 are a cause of autosomal dominant and autosomal recessive familial exudative vitreoretinopathy (FEVR). Autosomal dominant FEVR is also referred to as exudative vitreoretinopathy 1 (EVR1); also known as Criswick-Schepens syndrome. FEVR is a disorder of the retinal vasculature characterized by an低密度脂蛋白受体相关蛋白5抗体 abrupt cessation of growth of peripheral capillaries, leading to an avascular peripheral retina. This may lead to compensatory retinal neovascularization, which is thought to be induced by hypoxia from the initial avascular insult. New vessels are prone to leakage and rupture causing exudates and bleeding, followed by scarring, retinal detachment and blindness. FEVR is reported to have a penetrance of 100%, but clinical features can be highly variable,低密度脂蛋白受体相关蛋白5抗体 even within the same family. Patients with mild forms of the disease are asymptomatic, and their only disease-related abnormality is an arc of avascular retina in the extreme temporal periphery.
低密度脂蛋白受体相关蛋白5抗体Also known as:
BMND1; HBM; HGNC:6697; Low density lipoprotein receptor related protein 5; Low density lipoprotein receptor related protein 7; LR3; LRP7; OPPG; OPS; LRP7; Osteoporosis pseudoglioma syndrome; VBCH2; LRP5_HUMAN .
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
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Reacts with: Human, Mouse, Rat, Chicken, Dog, Cow, Horse, Rabbit, .
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Immunogen: KLH conjugated synthetic peptide derived from human LRP5.
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Predicted Molecular Weight: 176kDa.
低密度脂蛋白受体相关蛋白5抗体Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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kl518Mu01铁蛋白(FE)多克隆抗体Polyclonal Antibody to Ferritin (FE)
kl518Ra01铁蛋白(FE)多克隆抗体Polyclonal Antibody to Ferritin (FE)
kl355Hu01甲状腺球蛋白(TG)多克隆抗体Polyclonal Antibody to Thyroglobulin (TG)
kl355Mu01甲状腺球蛋白(TG)多克隆抗体Polyclonal Antibody to Thyroglobulin (TG)
kl355Ra01甲状腺球蛋白(TG)多克隆抗体Polyclonal Antibody to Thyroglobulin (TG)
kl821Mu01C反应蛋白(CRP)多克隆抗体Polyclonal Antibody to C Reactive Protein (CRP)
kl821Ra01C反应蛋白(CRP)多克隆抗体Polyclonal Antibody to C Reactive Protein (CRP)
kl216Hu01绒毛膜促性腺激素(CG)多克隆抗体Polyclonal Antibody to Chorionic Gonadotropin (CG)
kl930Hu01脱铁转铁蛋白(apoTf)多克隆抗体Polyclonal Antibody to Apotransferrin (apoTf)
kl037Hu01纤连蛋白(FN)多克隆抗体Polyclonal Antibody to Fibronectin (FN)
kl037Mu01纤连蛋白(FN)多克隆抗体Polyclonal Antibody to Fibronectin (FN)
kl037Ra01纤连蛋白(FN)多克隆抗体Polyclonal Antibody to Fibronectin (FN)
kl082Hu01层粘连蛋白(LN)多克隆抗体Polyclonal Antibody to Laminin (LN)
kl082Ra01层粘连蛋白(LN)多克隆抗体Polyclonal Antibody to Laminin (LN)
kl184Hu01粘蛋白21(MUC21)多克隆抗体Polyclonal Antibody to Mucin 21 (MUC21)
kl995Hu01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
kl995Mu01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
kl995Ra01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
kl995Bo01粘蛋白20(MUC20)多克隆抗体Polyclonal Antibody to Mucin 20 (MUC20)
kl403Hu01粘蛋白17(MUC17)多克隆抗体Polyclonal Antibody to Mucin 17 (MUC17)
kl403Bo01粘蛋白17(MUC17)多克隆抗体Polyclonal Antibody to Mucin 17 (MUC17)
kl808Hu01粘蛋白7(MUC7)多克隆抗体Polyclonal Antibody to Mucin 7, Secreted (MUC7)
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企业名称
上海康朗生物科技有限公司
企业信息已认证
企业类型
信用代码
310112001510759
成立日期
2015-05-29
注册资本
100
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上海康朗生物科技有限公司
公司地址
上海市闵行区闵北路88弄1-30号第22栋BV145室
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