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当前位置: 仪器信息网 > 康朗生物 > 抗体/抗原 > Beta氨基己糖苷酶beta亚基蛋白B链抗体

Beta氨基己糖苷酶beta亚基蛋白B链抗体

供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL15468R
CAS号:
报价: 面议
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产品介绍

Quantity size:

0.2ml

Concentration:

1mg/mlBeta氨基己糖苷酶beta亚基蛋白B链抗体   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

Hexosaminidase B is the beta subunit of the lysosomal enzyme beta-hexosaminidase that, together with the cofactor GM2 activator protein, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Beta-hexosaminidase is composed of two subunits, alpha and beta, which are encoded by separate genes.Beta氨基己糖苷酶beta亚基蛋白B链抗体 Both beta-hexosaminidase alpha and beta subunits are members of family 20 of glycosyl hydrolases. Mutations in the alpha or beta subunit genes lead to an accumulation of GM2 ganglioside in neurons and neurodegenerative disorders termed the GM2 gangliosidoses. Beta subunit gene mutations lead to Sandhoff disease (GM2-gangliosidosis type II). [provided by RefSeq, Jul 2008].

Beta氨基己糖苷酶beta亚基蛋白B链抗体Also known as:

Beta hexosaminidase beta chain; Beta hexosaminidase subunit beta; Beta N acetylhexosaminidase; Beta-hexosaminidase subunit beta chain B; Beta-N-acetylhexosaminidase subunit beta; Cervical cancer proto oncogene 7 protein; Cervical cancer proto-oncogene 7 protein; ENC 1AS; HCC 7; HCC-7; HCC7; HEX B; Hexb; HEXB_HUMAN; Hexosaminidase B (beta polypeptide); Hexosaminidase B; Hexosaminidase subunit B; HexosaminidaseB; N Beta氨基己糖苷酶beta亚基蛋白B链抗体acetyl beta glucosaminidase; N-acetyl-beta-glucosaminidase subunit beta; HEXB chain B.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Cow, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from human HEXB.

Beta氨基己糖苷酶beta亚基蛋白B链抗体Predicted Molecular Weight: 22/50kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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Beta氨基己糖苷酶beta亚基蛋白B链抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于Beta氨基己糖苷酶beta亚基蛋白B链抗体报价、型号、参数等信息,欢迎来电或留言咨询。除供应Beta氨基己糖苷酶beta亚基蛋白B链抗体外,上海康朗生物科技有限公司还可为您提供Beta氨基己糖苷酶beta亚基蛋白A链抗体等产品,公司有专业的客户服务团队,是您值得信赖的合作伙伴。
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