Quantity size:
0.2ml
Concentration:
1mg/ml 肌萎缩侧索硬化症相关蛋白HECW1抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
NEDL1 is a 1,606 amino acid cytoplasmic protein predominantly expressed in neurons of adult and fetal brain. NEDL1 functions as an E3 ubiquitin-protein ligase that, characteristic of E3 ligase proteins, accepts ubiquitin (in the form of a thioester) from an E2 ubiquitin-conjugating enzyme and transfers that ubiquitin residue to substrates targeted for 肌萎缩侧索硬化症相关蛋白HECW1抗体degradation. NEDL1 mediates ubiquitination and subsequent degradation of Dvl-1 and targets mutant SOD-1. NEDL1 forms cytotoxic aggregates with Dvl, TRAP-?and mutant SOD1 that lead to motor neuron death in FALS (familial amyotrophic lateral sclerosis). individuals affect by FALS (also known as Lou Gehrig's disease) experience muscle weakness and atrophy throughout the body. FALS is caused by the degeneration of upper and lower motor neurons resulting in loss of signal to muscles.
肌萎缩侧索硬化症相关蛋白HECW1抗体Also known as:
NEDL1; C2 and WW domain-containing protein 1; E3 ubiquitin-protein ligase HECW1; HECT; HECT type E3 ubiquitin ligase; HECT, C2 and WW domain containing E3 ubiquitin protein ligase 1; HECT, C2 and WW domain-containing protein 1; HECW 1; Hecw1; HECW1_HUMAN; hNEDL1; NEDD4 like ubiquitin protein ligase 1; NEDD4-like E3 ubiquitin-protein ligase 1; NEDL-1; NEDL 1.
Specificity:
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Rabbit Polyclonal IgG, 肌萎缩侧索硬化症相关蛋白HECW1抗体affinity purified by Protein A.
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Reacts with: Human, Mouse, Rat, Chicken, Dog, Cow, .
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Immunogen: KLH conjugated synthetic peptide derived from human HECW1 (2.
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Predicted Molecular Weight: 179kDa.
肌萎缩侧索硬化症相关蛋白HECW1抗体Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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kl277Ga01间隙连接蛋白43(CX43)多克隆抗体Polyclonal Antibody to Connexin 43 (CX43)
kl277Hu01间隙连接蛋白43(CX43)多克隆抗体Polyclonal Antibody to Connexin 43 (CX43)
kl277Mu01间隙连接蛋白43(CX43)多克隆抗体Polyclonal Antibody to Connexin 43 (CX43)
kl277Po01间隙连接蛋白43(CX43)多克隆抗体Polyclonal Antibody to Connexin 43 (CX43)
kl277Ra01间隙连接蛋白43(CX43)多克隆抗体Polyclonal Antibody to Connexin 43 (CX43)
kl277Rb51间隙连接蛋白43(CX43)多克隆抗体Polyclonal Antibody to Connexin 43 (CX43)
kl277Si01间隙连接蛋白43(CX43)多克隆抗体Polyclonal Antibody to Connexin 43 (CX43)
kl278Fi01踝蛋白(TLN)多克隆抗体Polyclonal Antibody to Talin (TLN)
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kl278Mu01踝蛋白(TLN)多克隆抗体Polyclonal Antibody to Talin (TLN)
kl280Hu01钙联蛋白(CNX)多克隆抗体Polyclonal Antibody to Calnexin (CNX)
kl281Ga01B-细胞激活因子受体(BAFFR)多克隆抗体Polyclonal Antibody to B-Cell Activation Factor Receptor (BAFFR)
kl281Hu01B-细胞激活因子受体(BAFFR)多克隆抗体Polyclonal Antibody to B-Cell Activation Factor Receptor (BAFFR)
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kl284Ga01肝素辅因子Ⅱ(HCⅡ)多克隆抗体Polyclonal Antibody to Heklin Cofactor II (HCII)
kl284Hu01肝素辅因子Ⅱ(HCⅡ)多克隆抗体Polyclonal Antibody to Heklin Cofactor II (HCII)
kl284Mu01肝素辅因子Ⅱ(HCⅡ)多克隆抗体Polyclonal Antibody to Heklin Cofactor II (HCII)
kl284Ra01肝素辅因子Ⅱ(HCⅡ)多克隆抗体Polyclonal Antibody to Heklin Cofactor II (HCII)
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企业名称
上海康朗生物科技有限公司
企业信息已认证
企业类型
信用代码
310112001510759
成立日期
2015-05-29
注册资本
100
经营范围
从事生物科技技术领域内技术开发、技术咨询、技术服务、技术转让,实验分析仪器、化工产品及原料(除危险化学品、监控化学品、烟花爆竹、民用爆竹物品、易制毒化学品)、仪器仪表、环保设备、酒店用品、皮革制品、床上用品、电子产品的销售。【依法须经批准的项目,经相关部门批准后方可开展经营活动】
上海康朗生物科技有限公司
公司地址
上海市闵行区闵北路88弄1-30号第22栋BV145室
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