Quantity size:
0.2ml
Concentration:
1mg/ml 长链烯脂酰辅酶A脱氢酶抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, 长链烯脂酰辅酶A脱氢酶抗体with the alpha subunit catalyzing the3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. [provided by RefSeq, Jul 2008].
长链烯脂酰辅酶A脱氢酶抗体Also known as:
HADHA; LCHAD; ECHA; GBP; HADH; LCEH; LCHAD; MTPA; TP-ALPHA; 3 ketoacyl Coenzyme A (CoA) thiolase alpha subunit; 3 oxoacyl CoA thiolase; 78 kDa gastrin binding protein; GBPv HADHv Hydroxyacyl Coenzyme A dehydrogenase/3 ketoacyl Coenzyme A thiolase/enoyl Coenzyme A hydratase (trifunctional protein) alpha subunit; LCHAD; Mitochondrial long chain 2 enoyl Coenzyme A (CoA) hydratase alpha subunit; Mitochondrial long chain L 3长链烯脂酰辅酶A脱氢酶抗体 hydroxyacyl Coenzyme A dehydrogenase alpha; Mitochondrial trifunctional enzyme alpha subunit; Mitochondrial trifunctional protein alpha subunit; MTPA; Thiolase/enoyl Coenzyme A
Specificity:
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Rabbit Polyclonal IgG, affinity purified by Protein A.
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长链烯脂酰辅酶A脱氢酶抗体Reacts with: Human, Mouse, Rat, Dog, Pig, Horse, Rabbit, .
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Immunogen: KLH conjugated synthetic peptide derived from human HADHA.
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Predicted Molecular Weight: 84kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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