Quantity size:
0.2ml
Concentration:
1mg/ml 脊髓性肌萎缩症蛋白Gemin6抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
Spinal muscular atrophy (SMA) is an autosomal recessive neurodegenerative disease characterized by loss of motor neurons in the spinal cord. SMA is caused by deletion or loss-of-function mutations in the SMN (Survival of Motor Neuron) gene. Gemin6, the protein product 脊髓性肌萎缩症蛋白Gemin6抗体of human chromosome 2p22.2, associates directly with SMN and is a part of the SMN complex containing Gemin2, Gemin3, Gemin4 and Gemin5 as well as several spliceosomal snRNP proteins. The SMN complex plays an essential role in spliceosomal snRNP assembly in the cytoplasm and is required for pre-mRNA splicing of the nucleus. The SMN complex is found in both the cytoplasm and the nucleus. The nuclear form is concentrated in subnuclear bodies called gems (Gemini of the coiled bodies).
脊髓性肌萎缩症蛋白Gemin6抗体Also known as:
FLJ23459; Gemin6; Gemin-6; Gem (nuclear organelle) associated protein 6; Gem-associated protein 6; GEMI6; GEMI6_HUMAN; Gemin-6; GEMIN6; SIP2.
Specificity:
●
Rabbit Polyclonal IgG, affinity purified by Protein A.
●
Reacts with: Human, 脊髓性肌萎缩症蛋白Gemin6抗体Mouse, Rat, Horse, Rabbit, .
●
Immunogen: KLH conjugated synthetic peptide derived from human Gemin 6.
●
Predicted Molecular Weight: 19kDa.
脊髓性肌萎缩症蛋白Gemin6抗体Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
kl035Hu01成纤维细胞生长因子6(FGF6)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor 6 (FGF6)
kl035Mu01成纤维细胞生长因子6(FGF6)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor 6 (FGF6)
kl035Ra01成纤维细胞生长因子6(FGF6)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor 6 (FGF6)
kl036Ga01成纤维细胞生长因子9(FGF9)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl036Hu01成纤维细胞生长因子9(FGF9)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl036Mu01成纤维细胞生长因子9(FGF9)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl036Po01成纤维细胞生长因子9(FGF9)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl036Ra01成纤维细胞生长因子9(FGF9)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor 9 (FGF9)
kl038Hu01FMS样酪氨酸激酶3配体(Flt3L)多克隆抗体Polyclonal Antibody to FMS Like Tyrosine Kinase 3 Ligand (Flt3L)
kl038Mu01FMS样酪氨酸激酶3配体(Flt3L)多克隆抗体Polyclonal Antibody to FMS Like Tyrosine Kinase 3 Ligand (Flt3L)
kl039Hu01FMS样酪氨酸激酶3(Flt3)多克隆抗体Polyclonal Antibody to FMS Like Tyrosine Kinase 3 (Flt3)
kl040Hu01趋化因子C-X3-C-基元配体1(CX3CL1)多克隆抗体Polyclonal Antibody to Chemokine C-X3-C-Motif Ligand 1 (CX3CL1)
kl040Mu01趋化因子C-X3-C-基元配体1(CX3CL1)多克隆抗体Polyclonal Antibody to Chemokine C-X3-C-Motif Ligand 1 (CX3CL1)
kl040Ra01趋化因子C-X3-C-基元配体1(CX3CL1)多克隆抗体Polyclonal Antibody to Chemokine C-X3-C-Motif Ligand 1 (CX3CL1)
kl041Hu01中性粒细胞激活蛋白3(NAP3)多克隆抗体Polyclonal Antibody to Neutrophil Activating Protein 3 (NAP3)
kl041Mu01中性粒细胞激活蛋白3(NAP3)多克隆抗体Polyclonal Antibody to Neutrophil Activating Protein 3 (NAP3)
kl041Ra01中性粒细胞激活蛋白3(NAP3)多克隆抗体Polyclonal Antibody to Neutrophil Activating Protein 3 (NAP3)
kl042Hu01粒细胞集落刺激因子(GCSF)多克隆抗体Polyclonal Antibody to Colony Stimulating Factor 3, Granulocyte (GCSF)
kl042Mu01粒细胞集落刺激因子(GCSF)多克隆抗体Polyclonal Antibody to Colony Stimulating Factor 3, Granulocyte (GCSF)
kl042Ra01粒细胞集落刺激因子(GCSF)多克隆抗体Polyclonal Antibody to Colony Stimulating Factor 3, Granulocyte (GCSF)
kl043Hu01胶质细胞系来源神经营养因子(GDNF)多克隆抗体Polyclonal Antibody to Glial Cell Line Derived Neurotrophic Factor (GDNF)
kl043Mu01胶质细胞系来源神经营养因子(GDNF)多克隆抗体Polyclonal Antibody to Glial Cell Line Derived Neurotrophic Factor (GDNF)
kl043Ra01胶质细胞系来源神经营养因子(GDNF)多克隆抗体Polyclonal Antibody to Glial Cell Line Derived Neurotrophic Factor (GDNF)
更多
企业名称
上海康朗生物科技有限公司
企业信息已认证
企业类型
信用代码
310112001510759
成立日期
2015-05-29
注册资本
100
经营范围
从事生物科技技术领域内技术开发、技术咨询、技术服务、技术转让,实验分析仪器、化工产品及原料(除危险化学品、监控化学品、烟花爆竹、民用爆竹物品、易制毒化学品)、仪器仪表、环保设备、酒店用品、皮革制品、床上用品、电子产品的销售。【依法须经批准的项目,经相关部门批准后方可开展经营活动】
上海康朗生物科技有限公司
公司地址
上海市闵行区闵北路88弄1-30号第22栋BV145室
客服电话