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当前位置: 仪器信息网 > 康朗生物 > 抗体/抗原 > 抗肌萎缩蛋白抗体

抗肌萎缩蛋白抗体

供货周期: 现货
品牌: 康朗生物
规格: 0.1ml/0.2ml
货号: KL14477R
CAS号:
报价: 面议
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产品介绍

Quantity size:

0.2ml

Concentration:

1mg/ml 抗肌萎缩蛋白抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

Dystotelin (DYTN) is a 578 amino acid cell membrane protein that contains one ZZ-type zinc finger. The gene that encodes dystrotelin maps to human chromosome 2, which makes up approximately 8% of the human genome and contains 237 million bases encoding over 1,400 genes. A number 抗肌萎缩蛋白抗体of genetic diseases are linked to genes on chromosome 2. Harlequin icthyosis, a rare skin deformity, is associated with mutations in the ABCA12 gene. The lipid metabolic disorder sitosterolemia is associated with ABCG5 and ABCG8. An extremely rare recessive genetic disorder, Alstr鰉 syndrome, 抗肌萎缩蛋白抗体is related to mutations in the ALMS1 gene. Chromosome 2 contains a probable vestigial second centromere as well as vestigial telomeres, which gives credence to the hypothesis that human chromosome 2 formed as a result of an ancient fusion of two ancestral chromosomes, which are still present in modern day apes.

Also known as:

抗肌萎缩蛋白抗体DMD_HUMAN; Dystrophin.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from human Dystroph.

抗肌萎缩蛋白抗体Predicted Molecular Weight: 426kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl527Hu01电子转移黄素蛋白α肽(ETFα)多克隆抗体Polyclonal Antibody to Electron Transfer Flavoprotein Alpha Polypeptide (ETFa)

kl536Hu01内皮细胞粘附分子(ESAM)多克隆抗体Polyclonal Antibody to Endothelial Cell Adhesion Molecule (ESAM)

kl544Hu01细胞粘附分子1(CADM1)多克隆抗体Polyclonal Antibody to Cell Adhesion Molecule 1 (CADM1)

kl562Mu01TATA框结合蛋白关联因子12(TAF12)多克隆抗体Polyclonal Antibody to TATA Box Binding Protein Associated Factor 12 (TAF12)

kl563Hu01TATA框结合蛋白关联因子13(TAF13)多克隆抗体Polyclonal Antibody to TATA Box Binding Protein Associated Factor 13 (TAF13)

kl564Hu01Tafazzin蛋白(TAZ)多克隆抗体Polyclonal Antibody to Tafazzin (TAZ)

kl569Ra01酶原颗粒膜糖蛋白(GP2)多克隆抗体Polyclonal Antibody to Glycoprotein 2, Zymogen Granule Membrane (GP2)

kl570Hu01α1-B-糖蛋白(α1BG)多克隆抗体Polyclonal Antibody to Alpha-1-B-Glycoprotein (a1BG)

kl571Hu01卷曲同源物1(FZD1)多克隆抗体Polyclonal Antibody to Frizzled Homolog 1 (FZD1)

kl576Hu01卷曲同源物6(FZD6)多克隆抗体Polyclonal Antibody to Frizzled Homolog 6 (FZD6)

kl593Hu01泛素关联蛋白2(UBAP2)多克隆抗体Polyclonal Antibody to Ubiquitin Associated Protein 2 (UBAP2)

kl594Hu01泛素结合酶E2C(UBE2C)多克隆抗体Polyclonal Antibody to Ubiquitin Conjugating Enzyme E2C (UBE2C)

kl624Mu01周期素依赖性激酶抑制因子1A(CDKN1A)多克隆抗体Polyclonal Antibody to Cyclin Dependent Kinase Inhibitor 1A (CDKN1A)

kl624Ra01周期素依赖性激酶抑制因子1A(CDKN1A)多克隆抗体Polyclonal Antibody to Cyclin Dependent Kinase Inhibitor 1A (CDKN1A)

kl645Hu01FK506结合蛋白5(FKBP5)多克隆抗体Polyclonal Antibody to FK506 Binding Protein 5 (FKBP5)

kl651Hu01微小染色体维持缺陷蛋白5(MCM5)多克隆抗体Polyclonal Antibody to Minichromosome Maintenance Deficient 5 (MCM5)

kl671Hu01SHC-转化蛋白1(SHC1)多克隆抗体Polyclonal Antibody to SHC-Transforming Protein 1 (SHC1)

kl673Hu01羟甲基胆素合酶(HMBS)多克隆抗体Polyclonal Antibody to Hydroxymethylbilane Synthase (HMBS)

kl674Hu01再生胰岛衍生蛋白1β(REG1β)多克隆抗体Polyclonal Antibody to Regenerating Islet Derived Protein 1 Beta (REG1b)

kl675Hu01再生胰岛衍生蛋白3α(REG3α)多克隆抗体Polyclonal Antibody to Regenerating Islet Derived Protein 3 Alpha (REG3a)

kl675Ra01再生胰岛衍生蛋白3α(REG3α)多克隆抗体Polyclonal Antibody to Regenerating Islet Derived Protein 3 Alpha (REG3a)



抗肌萎缩蛋白抗体信息由上海康朗生物科技有限公司为您提供,如您想了解更多关于抗肌萎缩蛋白抗体报价、型号、参数等信息,欢迎来电或留言咨询。除供应抗肌萎缩蛋白抗体外,上海康朗生物科技有限公司还可为您提供肌萎缩侧索硬化症相关蛋白2(2号染色体)抗体、肌萎缩侧索硬化症相关蛋白4抗体、肌萎缩Dystrobrevin β蛋白抗体等产品,公司有专业的客户服务团队,是您值得信赖的合作伙伴。
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上海康朗生物科技有限公司

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310112001510759

成立日期

2015-05-29

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100

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