β葡萄糖醛酸苷酶抗体

英文名称    beta glucuronidase    

中文名称    β葡萄糖醛酸苷酶抗体    

别    名    asd; Beta G1; Beta glucuronidase; Beta-G1; Beta-glucuronidase; BG; BGLR; BGLR_HUMAN; Glucuronidase beta; Gur; Gus; Gus-r; Gus-s; Gus-t; Gus-u; GUSB; Gut; MPS7; Ac2-223.    

说 明 书    0.1ml  0.2ml      

研究领域    细胞生物  免疫学  信号转导      

抗体来源    Rabbit    

克隆类型    Polyclonal    

交叉反应    Human, Mouse, Rat, Chicken, Dog, Pig, Cow,     

产品应用    WB=1:100-500 ELISA=1:500-1000 IP=1:20-100 IHC-P=1:100-500 IHC-F=1:100-500 IF=1:100-500 β葡萄糖醛酸苷酶抗体（石蜡切片需做抗原修复） 
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.    

分 子 量    69kDa    

细胞定位    细胞浆     

性    状    Lyophilized or Liquid    

浓    度    1mg/1ml    

免 疫 原    KLH conjugated synthetic peptide derived from human GUSB/beta glucuronidase    

亚    型    IgG    

纯化方法    affinity purified by Protein A    

储 存 液    Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4    

保存条件    Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.    

β葡萄糖醛酸苷酶抗体产品介绍    background:

Defects in GUSB are the cause of mucopolysaccharidosis type 7 (MPS7) ; also known as Sly syndrome. MPS7 is an autosomal recessive lysosomal storage disease characterized by inability to degrade glucuronic acid-containing glycosaminoglycans. The phenotype is highly variable, ranging from severe lethal hydrops fetalis to mild forms with survival into adulthood. Most patients with the intermediate phenotype show hepatomegaly, skeletal anomalies, coarse facies, and variable degrees of mental impairment. Mucopolysaccharidosis type 7 is associated with non-immune hydrops fetalis, a generalized edema of the fetus with fluid accumulation in the body cavities due to non-immune causes. Non-immune hydrops fetalis is not a diagnosis in itself but a symptom, a feature of many genetic disorders, and the end-stage of a wide variety of disorders.

Function:
Plays an important role in the degradation of dermatan and keratan sulfates.    

β葡萄糖醛酸苷酶抗体公司更多热销抗体产品如下：

hz-0901P MGr1-Ag/37LRP(P37-kDa laminin receptor precursor)(CT)  层粘连蛋白受体1抗原（C端）

hz-1849P MK(Midkine)  中期因子/肝素结合生长因子抗原

hz-2240P MLC/Myosin light chain 3 peptide  肌球蛋白轻链3抗原

hz-1044P MIF (Macrophage Migration Inhibitory Factor)  巨噬细胞移动抑制因子抗原

hz-1046P MIP-1 Beta (macrophage inflammatory protein 1 Beta)  巨噬细胞炎症因子1β 抗原

hz-1959P CD122/IL-2RB(Imterleukm-2 Receptor beta)  CD122/白介素2受体β链抗原

hz-1162P MIP2 (myocardial ischhzic preconditioning upregulated protein 2)  巨噬细胞炎症蛋白2抗原

hz-0575P MMP-13 (Matrix metalloproteinase 13)  基质金属蛋白酶13抗原

hz-0985P MMP-20(matrix metalloproteinase 20)  基质金属蛋白酶20抗原

hz-1862P MMP-17(Matrix metalloproteinase-17)  基质金属蛋白酶-17抗原

hz-1377P MMP-26(Matrix metalloproteinase-26)  基质金属蛋白酶-26抗原

hz-2099P MMP-9(matrix metalloproteinase 9)  基质金属蛋白酶-9抗原

hz-1344P MMP-10(matrix metalloproteinase 10)  基质金属蛋白酶-10抗原

hz-1061P MPO peptide  髓过氧化物酶抗原

hz-1092P MRP2 (multidrug resistance-associated protein2)  多药耐药相关蛋白2

hz-1437P MRP5/ABCC5(Multidrug Resistanec-Associated Protein 5)  多药耐药相关蛋白5抗原

hz-0818P MrpL28 (mitochondrial ribosomal protein L28)  线粒体核糖体蛋白L28(抗原)

hz-0836P MLH1(Mutl homolog l gene)  错配修复蛋白1抗原

hz-1022P MUC5AC/Mucin 5AC(Gastric Mucin M1)  胃粘液素抗原

hz-0963P MTNR1B/MTNR-1B(Melatonin receptor 1B)  褪黑素受体1B抗原

hz-1445P MLN(Motilin)peptide  胃动素多肽

hz-1992P mTOR(Mammalian target of rapamycin)  雷帕霉素靶蛋白

hz-1018P Muc-1/CD227  粘蛋白-1/上皮膜

hz-1047P MyD88 (myeloid differential protein-88)  髓样分化蛋白抗原

hz-2032P PMP2/FABP8(peripheral myelin protein 2)  周围神经髓鞘蛋白2抗原

hz-2166P MYSM1(Myb-like, SWIRM and MPN domain-containing protein 1)  MYSM1抗原

hz-1267P MYOZ/MYOZ1(Myozenin)human、ret、mouse  MYOZ抗原

hz-1049P CHRNA7(Nicotinic-Acetylcholine receptor alpha 7)  烟碱型乙酰胆碱受体α7(多肽)

hz-0829P Nanog fragment  干细胞关键蛋白(多肽)

hz-0903P Natrexone/BSA:Natrexone/KLH  纳曲酮偶联牛血清白蛋白：纳曲酮偶联血蓝蛋白