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Hermansky-Pudlak综合征蛋白1抗体

Hermansky-Pudlak综合征蛋白1抗体

价格: 面议

品牌:康朗生物

供货周期: 现货

货号:KL17379R

规格:0.1ml/0.2ml

Quantity size:

0.2ml

Concentration:

1mg/ml Hermansky-Pudlak综合征蛋白1抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

This gene encodes a protein that may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. The encoded protein is a component of three different protein complexes termed biogenesis of lysosome-related organelles complex (BLOC)-3, Hermansky-Pudlak综合征蛋白1抗体BLOC4, and BLOC5. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 1. Multiple transcript variants encoding distinct isoforms have been identified for this gene; the full-length sequences of some of these have not been determined yet. [provided by RefSeq, Jul 2008]

Hermansky-Pudlak综合征蛋白1抗体Also known as:

Hermansky Pudlak syndrome 1 protein; Hermansky Pudlak syndrome gene; Hermansky Pudlak syndrome type 1; Hermansky-Pudlak syndrome 1; Hermansky-Pudlak syndrome 1 protein; HPS; HPS1; HPS1_HUMAN; MGC5277.

Specificity:

Rabbit Polyclonal IgG,Hermansky-Pudlak综合征蛋白1抗体 affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Cow, Horse, .

Immunogen: KLH conjugated synthetic peptide derived from human HPS1.

Predicted Molecular Weight: 79kDa.

Hermansky-Pudlak综合征蛋白1抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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kl451Mu01早期生长应答因子2(EGR2)多克隆抗体Polyclonal Antibody to Early Growth Response Protein 2 (EGR2)

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生化试剂 Hermansky-Pudlak综合征蛋白1抗体由上海康朗生物科技有限公司为您提供,如想了解更多关于抗体/抗原 Hermansky-Pudlak综合征蛋白1抗体的报价、规格、厂家等信息,欢迎来电或留言咨询。除供应Hermansky-Pudlak综合征蛋白1抗体外,上海康朗生物科技有限公司还可为您提供: β-淀粉酶,9000-91-3、 干扰素调节因子3(IRF3)重组蛋白 、 山奈酚-3-鼠李糖苷,482-39-3
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