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溶酶体累积病相关蛋白/口吃相关蛋白抗体

溶酶体累积病相关蛋白/口吃相关蛋白抗体

价格: 面议

品牌:康朗生物

供货周期: 现货

货号:KL10460R

规格:0.1ml/0.2ml

Quantity size:

0.2ml

Concentration:

1mg/ml 溶酶体累积病相关蛋白/口吃相关蛋白抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

This gene encodes two of three subunit types of the membrane-bound enzyme N-acetylglucosamine-1-phosphotransferase, a heterohexameric complex composed of two alpha, two beta, and two gamma subunits. The encoded protein is proteolytically cleaved at the Lys928-Asp929 bond to 溶酶体累积病相关蛋白/口吃相关蛋白抗体yield mature alpha and beta polypeptides while the gamma subunits are the product of a distinct gene (GeneID 84572). In the Golgi apparatus, the heterohexameric complex catalyzes the first step in the synthesis of mannose 6-phosphate recognition markers on certain 溶酶体累积病相关蛋白/口吃相关蛋白抗体oligosaccharides of newly synthesized lysosomal enzymes. These recognition markers are essential for appropriate trafficking of lysosomal enzymes. Mutations in this gene have been associated with both mucolipidosis II and mucolipidosis IIIA.[provided by RefSeq, May 2010].

溶酶体累积病相关蛋白/口吃相关蛋白抗体Also known as:

N-acetylglucosamine-1-phosphotransferase subunit alpha; EC=2.7.8.17; GlcNAc-1-phosphotransferase subunits alpha/beta; GNPTA; GNPTA_HUMAN; Gnptab; KIAA1208; Stealth protein GNPTAB; UDP-N-acetylglucosamine-1-phosphotransferase subunits alpha/beta.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Pig, Cow, Horse, Rabbit, .

Immunogen: KLH conjugated synthetic peptide derived from human N-acetyl.

溶酶体累积病相关蛋白/口吃相关蛋白抗体Predicted Molecular Weight: 105kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

kl098Hu01基质金属蛋白酶10(MMP10)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 10 (MMP10)

kl098Mu01基质金属蛋白酶10(MMP10)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 10 (MMP10)

kl098Po01基质金属蛋白酶10(MMP10)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 10 (MMP10)

kl098Ra01基质金属蛋白酶10(MMP10)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 10 (MMP10)

kl099Bo01基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl099Ca01基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl099Cp01基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl099Eq01基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl099Ga01基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl099Hu01基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl099Mu01基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl099Po01基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl099Ra01基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl099Rb53基质金属蛋白酶13(MMP13)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 13 (MMP13)

kl100Hu01基质金属蛋白酶2(MMP2)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 2 (MMP2)

kl100Mu01基质金属蛋白酶2(MMP2)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 2 (MMP2)

kl100Ra01基质金属蛋白酶2(MMP2)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 2 (MMP2)

kl100Rb51基质金属蛋白酶2(MMP2)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 2 (MMP2)

kl101Bo01基质金属蛋白酶3(MMP3)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 3 (MMP3)

kl101Ca01基质金属蛋白酶3(MMP3)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 3 (MMP3)

kl101Eq01基质金属蛋白酶3(MMP3)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 3 (MMP3)

kl101Hu01基质金属蛋白酶3(MMP3)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 3 (MMP3)

kl101Mu01基质金属蛋白酶3(MMP3)多克隆抗体Polyclonal Antibody to Matrix Metalloproteinase 3 (MMP3)





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