找不到产品？留下需求帮您找
一键询价
-
德国耶拿 multi N/C 3100 TOC总有机碳/总氮分析仪型号： multi N/C 3100 -
瑞士万通Multi Autolab/M204多通道电化学工作站型号： Multi Autolab/M204 -
德国FRITSCH P7 小型行星式球磨机/仪加强型型号： PULVERISETTE 7 premium line -
激光干涉仪型号： XL80 -
Hitachi日立CT15RE台式离心机型号： CT15RE -
Hitachi日立超速离心机CP70ME型号： CP70ME -
电热鼓风干燥箱型号： CS101-ABN -
Agilent 8890 气相色谱系统型号： 8890 GC -
日立Primaide PLUS高效液相色谱仪型号： Primaide PLUS
获取电话Quantity size:
0.2ml
Concentration:
1mg/ml 氨基葡萄糖6-硫酸酯酶抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
GNS is a 552 amino acid lysosomal enzyme that hydrolyzes the 6-sulfate groups of the N-acetyl-D-glucosamine 6-sulfate units of keratan sulfate and heparan sulfate. A member of the sulfatase family, GNS assists in the catabolism of heparin, and binds calcium as a cofactor. GNS 氨基葡萄糖6-硫酸酯酶抗体deficiency results in an autosomal recessive lysosomal storage disorder known as mucopolysaccharidosis type IIID (Sanfilippo D syndrome), which is characterized by mild somatic disease and severe degeneration of the central nervous system. Subject to post-translational internal peptidase cleavage, GNS is encoded by a gene mapping to human chromosome 12q14.2 and mouse chromosome 10 D2.
氨基葡萄糖6-硫酸酯酶抗体Also known as:
2610016K11Rik; AU042285; C87209; G6S; Glucosamine (N-acetyl) 6 sulfatase; Glucosamine 6 sulfatase; Glucosamine-6-sulfatase; GNS; GNS_HUMAN; MGC21274; N acetylglucosamine 6 sulfatase [Precursor]; N-acetylglucosamine-6-sulfatase; N28088.
Specificity:
●
Rabbit Polyclonal IgG,氨基葡萄糖6-硫酸酯酶抗体 affinity purified by Protein A.
●
Reacts with: Human, Mouse, Rat, Cow, Horse, Rabbit, .
●
Immunogen: KLH conjugated synthetic peptide derived from human GNS/Gluc.
●
Predicted Molecular Weight: 58kDa.
氨基葡萄糖6-硫酸酯酶抗体Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
kl799Hu01成纤维细胞生长因子受体4(FGFR4)多克隆抗体Polyclonal Antibody to Fibroblast Growth Factor Receptor 4 (FGFR4)
kl801Hu01激肽释放酶原(PK)多克隆抗体Polyclonal Antibody to Prekallikrein (PK)
kl802Hu01白介素32(IL32)多克隆抗体Polyclonal Antibody to Interleukin 32 (IL32)
kl807Hu01Jagged 1蛋白(JAG1)多克隆抗体Polyclonal Antibody to Jagged 1 Protein (JAG1)
kl807Mu01Jagged 1蛋白(JAG1)多克隆抗体Polyclonal Antibody to Jagged 1 Protein (JAG1)
kl812Hu01β-位淀粉样前体蛋白裂解酶2(βACE2)多克隆抗体Polyclonal Antibody to Beta-Site APP Cleaving Enzyme 2 (bACE2)
kl815Hu01白介素6受体(IL6R)多克隆抗体Polyclonal Antibody to Interleukin 6 Receptor (IL6R)
kl815Mu01白介素6受体(IL6R)多克隆抗体Polyclonal Antibody to Interleukin 6 Receptor (IL6R)
kl815Ra01白介素6受体(IL6R)多克隆抗体Polyclonal Antibody to Interleukin 6 Receptor (IL6R)
kl817Hu01多功能蛋白聚糖(VS)多克隆抗体Polyclonal Antibody to Versican (VS)
kl817Mu01多功能蛋白聚糖(VS)多克隆抗体Polyclonal Antibody to Versican (VS)
kl818Mu01血管内皮生长因子受体1(VEGFR1)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor Receptor 1 (VEGFR1)
kl818Ra01血管内皮生长因子受体1(VEGFR1)多克隆抗体Polyclonal Antibody to Vascular Endothelial Growth Factor Receptor 1 (VEGFR1)
kl819Mu01再生胰岛衍生蛋白4(REG4)多克隆抗体Polyclonal Antibody to Regenerating Islet Derived Protein 4 (REG4)
kl822Hu01角蛋白17(KRT17)多克隆抗体Polyclonal Antibody to Keratin 17 (KRT17)
kl823Hu01补体成分9(C9)多克隆抗体Polyclonal Antibody to Complement Component 9 (C9)
kl823Ra01补体成分9(C9)多克隆抗体Polyclonal Antibody to Complement Component 9 (C9)
kl824Ga01核因子κB(NFκB)多克隆抗体Polyclonal Antibody to Nuclear Factor Kappa B (NFkB)
kl824Hu01核因子κB(NFκB)多克隆抗体Polyclonal Antibody to Nuclear Factor Kappa B (NFkB)
kl824Mu01核因子κB(NFκB)多克隆抗体Polyclonal Antibody to Nuclear Factor Kappa B (NFkB)
kl824Ra01核因子κB(NFκB)多克隆抗体Polyclonal Antibody to Nuclear Factor Kappa B (NFkB)
kl825Mu01核因子κB2(NFκB2)多克隆抗体Polyclonal Antibody to Nuclear Factor Kappa B2 (NFkB2)
kl826Hu01V-Rel网状内皮增生病毒癌基因同源物B(RELB)多克隆抗体Polyclonal Antibody to V-Rel Reticuloendotheliosis Viral Oncogene Homolog B (RELB)
