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溶酶体累积病相关蛋白/口吃相关蛋白抗体

溶酶体累积病相关蛋白/口吃相关蛋白抗体

价格: 面议

品牌:康朗生物

供货周期: 现货

货号:KL13476R

规格:0.1ml/0.2ml

Quantity size:

0.2ml

Concentration:

1mg/ml 溶酶体累积病相关蛋白/口吃相关蛋白抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

This gene encodes two of three subunit types of the membrane-bound enzyme N-acetylglucosamine-1-phosphotransferase, a heterohexameric complex composed of two alpha, two beta, and two gamma subunits. The encoded protein is proteolytically cleaved at the Lys928-Asp929 bond to yield mature alpha and beta polypeptides while the gamma subunits are the product 溶酶体累积病相关蛋白/口吃相关蛋白抗体of a distinct gene (GeneID 84572). In the Golgi apparatus, the heterohexameric complex catalyzes the first step in the synthesis of mannose 6-phosphate recognition markers on certain oligosaccharides of newly synthesized lysosomal enzymes. These recognition markers are essential for appropriate trafficking of lysosomal enzymes. Mutations in this gene have been associated with both mucolipidosis II and mucolipidosis IIIA.[provided by RefSeq, May 2010].

溶酶体累积病相关蛋白/口吃相关蛋白抗体Also known as:

N-acetylglucosamine-1-phosphotransferase subunit beta; EC=2.7.8.17; GlcNAc-1-phosphotransferase subunits alpha/beta; GNPTA; GNPTA_HUMAN; Gnptab; KIAA1208; Stealth protein GNPTAB; UDP-N-acetylglucosamine-1-phosphotransferase subunits alpha/beta.

Specificity:

Rabbit Polyclonal IgG,溶酶体累积病相关蛋白/口吃相关蛋白抗体 affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from human N-acetyl.

Predicted Molecular Weight: 39kDa.

溶酶体累积病相关蛋白/口吃相关蛋白抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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kl750Hu01肿瘤坏死因子配体超家族成员13(TNFSF13)多克隆抗体Polyclonal Antibody to Tumor Necrosis Factor Ligand Superfamily, Member 13 (TNFSF13)

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kl760Hu01再生胰岛衍生蛋白1α(REG1α)多克隆抗体Polyclonal Antibody to Regenerating Islet Derived Protein 1 Alpha (REG1a)

kl760Ra01再生胰岛衍生蛋白1α(REG1α)多克隆抗体Polyclonal Antibody to Regenerating Islet Derived Protein 1 Alpha (REG1a)

kl761Hu01抑瘤素M受体(OSMR)多克隆抗体Polyclonal Antibody to Oncostatin M Receptor (OSMR)

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kl766Mu01可溶性半乳糖凝集素3结合蛋白(LGALS3BP)多克隆抗体Polyclonal Antibody to Lectin Galactoside Binding, Soluble 3 Binding Protein (LGALS3BP)

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kl769Hu01S100钙结合蛋白A6(S100A6)多克隆抗体Polyclonal Antibody to S100 Calcium Binding Protein A6 (S100A6)





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