Quantity size:
0.2ml
Concentration:
1mg/ml GDP甘露糖焦磷酸化酶B抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
GMPPB is a 360 amino acid protein that belongs to the transferase hexapeptide repeat family and is involved in protein modification pathways. Functioning as a GDP-mannose pyrophosphorylase, GMPPB enzymatically catalyzes the conversion of mannose-1-phosphate and GTP to GDP-mannose and a free phosphate, a reaction that is involved in the production of GDP甘露糖焦磷酸化酶B抗体N-linked oligosaccharides. Defects in the gene encoding GMPPB that cause errors in the glycosylation pathway may lead to congenital disorders of glycosylation (CDG). CDGs are multisystemic diseases that often involve both the central and peripheral nervous systems and are often characterized by endocrine and coagulation disorders. GMPPB is expressed as two isoforms due to alternative splicing events.
GDP甘露糖焦磷酸化酶B抗体Also known as:
GDP mannose pyrophosphorylase B; GDP-mannose pyrophosphorylase B; GMPPB; GMPPB_HUMAN; GTP-mannose-1-phosphate guanylyltransferase beta; KIAA1851; Mannose 1 phosphate guanylyltransferase; Mannose-1-phosphate guanyltransferase beta.
Specificity:
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Rabbit Polyclonal IgG, GDP甘露糖焦磷酸化酶B抗体affinity purified by Protein A.
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Reacts with: Human, Mouse, Rat, Pig, Cow, Horse, Rabbit, Sheep, .
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Immunogen: KLH conjugated synthetic peptide derived from human GMPPB.
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Predicted Molecular Weight: 40kDa.
GDP甘露糖焦磷酸化酶B抗体Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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GDP甘露糖焦磷酸化酶B抗体多少钱?
康朗生物抗体/抗原的应用资料有吗?
康朗生物抗体/抗原货号KL13461R报价含票含运吗?
康朗生物货号KL13461R货期是多久?
康朗生物GDP甘露糖焦磷酸化酶B抗体可以申请试用吗?
康朗生物康朗生物抗体/抗原售后政策是什么?
GDP甘露糖焦磷酸化酶B抗体有现货吗?