Quantity size:
0.2ml
Concentration:
1mg/ml 半乳糖瓦尔登转化酶抗体 Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.
Background:
This gene encodes UDP-galactose-4-epimerase which catalyzes two distinct but analogous reactions: the epimerization of UDP-glucose to UDP-galactose, and the epimerization of UDP-N-acetylglucosamine to UDP-N-acetylgalactosamine. The bifunctional nature of the enzyme has the important metabolic consequence that mutant cells (or individuals) are半乳糖瓦尔登转化酶抗体 dependent not only on exogenous galactose, but also on exogenous N-acetylgalactosamine as a necessary precursor for the synthesis of glycoproteins and glycolipids. Mutations in this gene result in epimerase-deficiency galactosemia, also referred to as galactosemia type 3, a 半乳糖瓦尔登转化酶抗体disease characterized by liver damage, early-onset cataracts, deafness and mental retardation, with symptoms ranging from mild ('peripheral' form) to severe ('generalized' form). Multiple alternatively spliced transcripts encoding the same protein have been identified. [provided by RefSeq, Jul 2008]
Also known as:
FLJ95174; FLJ97302; Galactose 4 epimerase UDP; Galactowaldenase; galE; GALE_HUMAN; OTTHUMP00000002991; OTTHUMP00000002994; OTTHUMP00000037931; OTTHUMP00000044857; SDR1E1; short chain dehydrogenase/reductase family 1E member 1; UDP galactose 4 epimerase; UDP glucose 4 epimerase;半乳糖瓦尔登转化酶抗体 UDP-galactose 4-epimerase; UDP-glucose 4-epimerase.
Specificity:
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Rabbit Polyclonal IgG, affinity purified by Protein A.
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Reacts with: Human, Mouse, Rat, Pig, Horse, .
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Immunogen: KLH conjugated synthetic peptide derived from human GALE/Gal.
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半乳糖瓦尔登转化酶抗体Predicted Molecular Weight: 38kDa.
Storage:
Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).
Application:
WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
Not yet tested in other applications.
Optimal working dilutions must be determined by the end user.
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半乳糖瓦尔登转化酶抗体多少钱?
康朗生物抗体/抗原的应用资料有吗?
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康朗生物货号KL13265R货期是多久?
康朗生物半乳糖瓦尔登转化酶抗体可以申请试用吗?
康朗生物康朗生物抗体/抗原售后政策是什么?
半乳糖瓦尔登转化酶抗体有现货吗?