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强直性肌营养不良相关蛋白9抗体

强直性肌营养不良相关蛋白9抗体

价格: 面议

品牌:康朗生物

供货周期: 现货

货号:KL13042R

规格:0.1ml/0.2ml

Quantity size:

0.2ml

Concentration:

1mg/ml 强直性肌营养不良相关蛋白9抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

DMWD is a 674 amino acid protein containing five WD repeats. DMWD may play a role in the development of mental symptoms in severe cases of myotonic dystrophy, a chronic multisystemic disease characterized by wasting of the muscles, heart conduction defects, cataracts, 强直性肌营养不良相关蛋白9抗体endocrine changes and myotonia. The DMWD gene is located upstream of the DMPK gene and is prominently expressed in tissues affected in myotonic dystrophy patients. DMWD may also contribute to regulation in meiosis. DMWD is expressed in kidney and spleen, with strongest expression in brain, liver and testis. The gene encoding DMWD maps to human chromosome 19q13.32 and mouse chromosome 7 A3.

强直性肌营养不良相关蛋白9抗体Also known as:

dystrophia myotonica containing WD repeat motif; D19S593E; DM 9; DM9; DMR N9; DMR N9 protein; DMRN 9; DMRN9; DMWD; DMWD_HUMAN; Dystrophia myotonica containing WD repeat motif; Dystrophia myotonica containing WD repeat motif protein; Dystrophia myotonica WD repeat containing protein; 强直性肌营养不良相关蛋白9抗体Dystrophia myotonica WD repeat-containing protein; Dystrophia myotonica-containing WD repeat motif protein; Gene59; Protein 59; Protein DMR-N9.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Cow, .

Immunogen: KLH conjugated synthetic peptide derived from human DMWD/DMR.

强直性肌营养不良相关蛋白9抗体Predicted Molecular Weight: 70kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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生化试剂 强直性肌营养不良相关蛋白9抗体由上海康朗生物科技有限公司为您提供,如想了解更多关于抗体/抗原 强直性肌营养不良相关蛋白9抗体的报价、规格、厂家等信息,欢迎来电或留言咨询。除供应强直性肌营养不良相关蛋白9抗体外,上海康朗生物科技有限公司还可为您提供: β-淀粉酶,9000-91-3、 干扰素调节因子3(IRF3)重组蛋白 、 山奈酚-3-鼠李糖苷,482-39-3
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