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软骨衍生形态发生蛋白1/GDF 5抗体

软骨衍生形态发生蛋白1/GDF 5抗体

价格: 面议

品牌:康朗生物

供货周期: 现货

货号:KL6580R

规格:0.1ml/0.2ml

Quantity size:

0.2ml

Concentration:

1mg/ml 软骨衍生形态发生蛋白1/GDF 5抗体  Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

Defects in GDF5 are the cause of acromesomelic chondrodysplasia Grebe type (AMDG) . Acromesomelic chondrodysplasias are rare hereditary skeletal disorders characterized by short stature, very short limbs, and hand/foot malformations. The severity of limb abnormalities increases from proximal to distal with profoundly affected hands and feet showing brachydactyly and/or rudimentary fingers 软骨衍生形态发生蛋白1/GDF 5抗体(knob-like fingers). AMDG is an autosomal recessive form characterized by normal axial skeletons and missing or fused skeletal elements within the hands and feet. Defects in GDF5 are the cause of acromesomelic chondrodysplasia Hunter-Thompson type (AMDH). AMDH is an autosomal recessive form of dwarfism. Patients have limb abnormalities, with the middle and distal segments being most affected and the lower limbs more affected than the upper.软骨衍生形态发生蛋白1/GDF 5抗体 AMDH is characterized by normal axial skeletons and missing or fused skeletal elements within the hands and feet. Defects in GDF5 are the cause of brachydactyly type C (BDC). BDC is an autosomal dominant disorder characterized by an abnormal shortness of the fingers and toes.

Also known as:

Cartilage derived morphogenetic protein 1; Cartilage-derived morphogenetic protein 1; CDMP-1; CDMP1; GDF-5; Gdf 5; GDF5_HUMAN; Growth differentiation factor 5; Growth/differentiation factor 5; LAP4; 软骨衍生形态发生蛋白1/GDF 5抗体Radotermin.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Horse, Rabbit, .

Immunogen: KLH conjugated synthetic peptide derived from human CDMP1/GDF5.

软骨衍生形态发生蛋白1/GDF 5抗体Predicted Molecular Weight: 55kDa.

Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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生化试剂 软骨衍生形态发生蛋白1/GDF 5抗体由上海康朗生物科技有限公司为您提供,如想了解更多关于抗体/抗原 软骨衍生形态发生蛋白1/GDF 5抗体的报价、规格、厂家等信息,欢迎来电或留言咨询。除供应软骨衍生形态发生蛋白1/GDF 5抗体外,上海康朗生物科技有限公司还可为您提供: β-淀粉酶,9000-91-3、 干扰素调节因子3(IRF3)重组蛋白 、 山奈酚-3-鼠李糖苷,482-39-3
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