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遗传性失明相关蛋白AIPL1抗体

遗传性失明相关蛋白AIPL1抗体

价格: 1

品牌:康朗生物

供货周期: 现货

货号:KL12452R

规格:0.1ml/0.2ml

?遗传性失明相关蛋白AIPL1抗体Quantity size:

0.2ml

Concentration:

1mg/ml   Buffer = 0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

Background:

The inherited blindness associated protein, aryl hydrocarbon receptor interacting protein-like 1 (AIPL1), interacts with the cell cycle regulator protein NUB1. AIPL1 is crucial for protein folding and stabilization, as well as for protein trafficking. It localizes to the nucleus or cytoplasm and is highly expressed in the pineal gland and the retina. In the retina,遗传性失明相关蛋白AIPL1抗体AIPL1 is expressed in both developing cone and rod photoreceptors, but it is restricted to rod photoreceptors in the adult human retina. Defects in the gene encoding for AIPL1 can cause Leber congenital amaurosis type IV, an early-onset, inherited autosomal recessive disorder that results in childhood blindness.

遗传性失明相关蛋白AIPL1抗体Also known as:

A930007I01Rik; Aipl1; AIPL1_HUMAN; AIPL2; Aryl hydrocarbon interacting protein like 1; Aryl hydrocarbon receptor interacting protein like 1; Aryl-hydrocarbon-interacting protein-like 1; LCA4; MGC25485;遗传性失明相关蛋白AIPL1抗体 OTTHUMP00000128207; OTTMUSP00000006382; RP23-401C17.1.

Specificity:

Rabbit Polyclonal IgG, affinity purified by Protein A.

Reacts with: Human, Mouse, Rat, Dog, Pig, Cow, Rabbit, Sheep, .

Immunogen: KLH conjugated synthetic peptide derived from human AIPL1.

Predicted Molecular Weight: 44kDa.

遗传性失明相关蛋白AIPL1抗体Storage:

Shipped at 4℃, Store at -20℃ (Avoid repeated freeze/thaw cycles).

Application:

WB=1:100-500  ELISA=1:500-1000  IHC-P=1:100-500  IHC-F=1:100-500  ICC=1:100-500  IF=1:100-500   
Not yet tested in other applications. 
Optimal working dilutions must be determined by the end user.

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生化试剂 遗传性失明相关蛋白AIPL1抗体由上海康朗生物科技有限公司为您提供,如想了解更多关于抗体/抗原 遗传性失明相关蛋白AIPL1抗体的报价、规格、厂家等信息,欢迎来电或留言咨询。除供应遗传性失明相关蛋白AIPL1抗体外,上海康朗生物科技有限公司还可为您提供: β-淀粉酶,9000-91-3、 干扰素调节因子3(IRF3)重组蛋白 、 山奈酚-3-鼠李糖苷,482-39-3
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