兔抗AAAS多克隆抗体
中文名称: 兔抗AAAS多克隆抗体
英文名称: Anti-AAAS rabbit polyclonal antibody
别 名: AAA; AAASb; GL003; ALADIN; ADRACALA; ADRACALIN
相关类别: 一抗
储 存: 冷冻(-20℃)
抗 原: AAAS
宿 主: Rabbit
反应种属: Human, Mouse
标 记 物: Unconjugate
克隆类型: rabbit polyclonal
技术规格: 兔抗AAAS多克隆抗体
Background: | The protein encoded by this gene is a member of the WD-repeat family of regulatory proteins and may be involved in normal development of the peripheral and central nervous system. The encoded protein is part of the nuclear pore complex and is anchored there by NDC1. Defects in this gene are a cause of achalasia-addisonianism-alacrima syndrome (AAAS), also called triple-A syndrome or Allgrove syndrome. Two transcript variants encoding different isoforms have been found for this gene. |
Applications: | ELISA, IHC |
Name of antibody: | AAAS |
Immunogen: | Fusion protein of human AAAS |
Full name: | achalasia, adrenocortical insufficiency, alacrimia |
Synonyms: | AAA; AAASb; GL003; ALADIN; ADRACALA; ADRACALIN |
SwissProt: | Q9NRG9 |
ELISA Recommended dilution: | 1000-2000 |
IHC positive control: | Human breast cancer and Human brain |
IHC Recommend dilution: | 25-100 |
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