英文名称 ETFDH
中文名称 电子转移黄素蛋白脱氢酶抗体
别 名 Electron transfer flavoprotein ubiquinone oxidoreductase; Electron transfer flavoprotein-ubiquinone oxidoreductase; electron transferring flavoprotein dehydrogenase; Electron-transferring-flavoprotein dehydrogenase; ETF dehydrogenase; ETF QO; ETF ubiquinone oxidoreductase; ETF-QO; ETF-ubiquinone oxidoreductase; ETFD_HUMAN; Etfdh; mitochondrial.
说 明 书 0.2ml
研究领域 细胞生物 信号转导 细胞类型标志物 新陈代谢
抗体来源 Rabbit
克隆类型 Polyclonal
交叉反应 Human, Mouse, Rat, Chicken, Dog, Horse, Rabbit,
产品应用 WB=1:100-500 ELISA=1:500-1000 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500 电子转移黄素蛋白脱氢酶抗体(石蜡切片需做抗原修复)
not yet tested in other applications.
optimal dilutions/concentrations should be determined by the end user.
分 子 量 65kDa
细胞定位 细胞浆 细胞膜
性 状 Lyophilized or Liquid
浓 度 1mg/1ml
免 疫 原 KLH conjugated synthetic peptide derived from human ETFDH
亚 型 IgG
纯化方法 affinity purified by Protein A
储 存 液 Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4
保存条件 Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C.
电子转移黄素蛋白脱氢酶抗体产品介绍 background:
Electron-transferring-flavoprotein dehydrogenase in the inner mitochondrial membrane accepts electrons from electron-transfer flavoprotein which is located in the mitochondrial matrix and reduces ubiquinone in the mitochondrial membrane. The protein is synthesized as a 67-kDa precursor which is targeted to mitochondria and processed in a single step to a 64-kDa mature form located in the mitochondrial membrane. Deficiency in electron-transferring-flavoprotein dehydrogenase have been demonstrated in some patients with type II glutaricacidemia. [provided by RefSeq, Jul 2008].
Function:
Accepts electrons from ETF and reduces ubiquinone.
Subunit:
Monomer.
Subcellular Location:
Mitochondrion inner membrane.
DISEASE:
Defects in ETFDH are the cause of glutaric aciduria type 2C (GA2C) [MIM:231680]. GA2C is an autosomal recessively inherited disorder of fatty acid, amino acid, and choline metabolism. It is characterized by multiple acyl-CoA dehydrogenase deficiencies resulting in large excretion not only of glutaric acid, but also of lactic, ethylmalonic, butyric, isobutyric, 2-methyl-butyric, and isovaleric acids.
Similarity:
Belongs to the ETF-QO/fixC family.
Contains 1 4Fe-4S ferredoxin-type domain.
Database links:
UniProtKB/Swiss-Prot: Q16134.2
Important Note:
This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications.
电子转移黄素蛋白脱氢酶抗体
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hz-0133P PP-1 蛋白磷酸酯酶-1(抗原)
hz-1509P BMPR-1A(Bone Morphogenetic protein Receptor-1A) 骨成型蛋白受体1A抗原
hz-0250P PPAR-delta (peroxisome proliferator-activated receptor) D型-过氧化酶活化增生受体(多肽)
hz-0029P PP-2A (protein phosphatase 2A) 蛋白质磷酸酶-2A(抗原)
hz-1418P BOb-1(B-cell oct-binding protein 1) B细胞特异性转录因子抗原
hz-0030P PP-2B alpha 1 蛋白磷酸酯酶-2B 催化亚单位(抗原)
hz-0111P PR (Progestogerone receptor) 孕激素受体(抗原)
hz-0024P PS-1(NT),Presennillin-1(S182) 早老素蛋白-1(抗原)
hz-0025P PS-1,Presennillin-1(CT) 早老素蛋白-1(S182)
hz-0803P BRCA1(Breast cancer susceptbility gene 1)(mouse rat) 乳腺癌易感基因1抗原(小鼠 大鼠)
hz-0802P BRCA1 乳腺癌易感基因1抗原
hz-0179P PSD-95 突触后密度蛋白95(抗原)
hz-1210P BRCA2(Breast cancer susceptbility gene 2) 乳腺癌易感基因2抗原
hz-0182P PTP-1B (Protein-tyrosine phosphatase, non-receptor ) 蛋白酪氨酸磷酸酶-1B(抗原)
hz-0251P RAR-Alpha (Retinoic acid -R-Alpha) 维甲酸受体-α 多肽
hz-0319P glycoprotein (E1 glycoprotein) [Rubella virus] 风疹病毒糖蛋白多肽片段
hz-0121P SAP-1 (Synapse associated protein-I) peptide 突触相关蛋白-1(多肽抗原)
hz-0130P SARS S-protein(抗原)
hz-0132P SARS putative orflab polyprotein (SARS coronavirus CUHK-W1)(抗原)
hz-4813-P 禽流感H5亚型全病毒抗原 H5N1-H5
hz-1954P BSEP peptide 胆汁酸盐输出泵蛋白抗原
hz-0088P Secretin 分泌素(抗原)
hz-0089P Secretin receptor 分泌素受体(抗原)
hz-0113P Socs 1 (suppressor of cytokine signaling 1) 细胞激酶信号-1抑制剂(抗原)
hz-0259P SM-MHC(Cardiac myosin heavy chain) 心肌肌凝蛋白多肽
hz-0009P Alpha-Synuclein 核突触蛋白(抗原)
hz-0012P Alpha-Synuclein 核突触蛋白(抗原)
hz-1239P CA15-3 peptide 乳腺癌相关抗原抗原
hz-0064P Substance P Receptor (Neurokinin receptor1;Tachykinin receptor1) P物质受体(抗原)
hz-2082P p-Caldesmon(phosphor-Ser789) 磷酸化钙介质素抗原
hz-0123P NK-2R peptide 神经激肽A受体(多肽抗原)
hz-1099P Calpain 1 钙蛋白酶(多肽)
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